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The multistep hypothesis of ALS revisited
Adriano Chiò
, Letizia Mazzini
,
Sandra D'Alfonso
,
Lucia Corrado
, Antonio Canosa
, Cristina Moglia
, Umberto Manera
, Enrica Bersano
, Maura Brunetti
, Marco Barberis
, Jan H. Veldink
, Leonard H. Van Den Berg
, Neil Pearce
, William Sproviero
, Russell McLaughlin
, Alice Vajda
, Orla Hardiman
, James Rooney
, Gabriele Mora
, Andrea Calvo
Ammar Al-Chalabi
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Dipartimento di Scienze della Salute
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Keyphrases
Amyotrophic Lateral Sclerosis
100%
Step Processes
30%
TARDBP Gene
20%
Linear Relationship
20%
Multi-step Process
20%
Italy
10%
Incidence Rate
10%
Incidence Data
10%
Genetic mutation
10%
Genetic Analysis
10%
TARDBP
10%
Superoxide Dismutase 1 (SOD1)
10%
Disease-associated
10%
Incident Cases
10%
Whole Population
10%
4-step
10%
Pathogenic Process
10%
C9ORF72 Gene
10%
C9orf72
10%
Age-specific Incidence
10%
FUS Gene
10%
SOD1 Gene
10%
Number of Steps
10%
C9orf72 mutation
10%
SOD1 mutation
10%
3-step
10%
Population Register
10%
1-step
10%
FUS mutation
10%
Least Squares Regression
10%
2-step Process
10%
Republic of Ireland
10%
Biochemistry, Genetics and Molecular Biology
TARDBP
100%
SOD1
100%
C9orf72
100%
FUS
66%
Gene Mutation
33%
Genetics
33%
Mathematics
Step Process
100%
Slope Estimate
75%
Linear Relationship
50%
Incidence Rate
25%
Least Square
25%
Subpopulation
25%
Square Regression
25%
Agricultural and Biological Sciences
SOD1
100%
TARDBP
100%
FUS
66%
Least Square
33%
Immunology and Microbiology
Gene Mutation
100%